hrp0092p2-22 | Adrenals and HPA Axis | ESPE2019

An Atypical Case of Ectopic ACTH Syndrome in an Adolescent Boy

Sharma Shreya , Joshi Rajesh

Background: Ectopic ACTH syndrome (EAS) is exceedingly rare in children and scarcely reported. Pancreatic Neuroendocrine tumours (NET) can rarely lead to secretion of ectopic adrenocorticotropic hormone (ACTH).Case Characteristics: A14-year-old adolescent boy presented with isolated hyperpigmentation and intermittent abdominal pain and underwent evaluation for primary adrenal insufficiency, but turned out to have subclin...